Tuesday, August 13, 2013

Cardiovascular Malformations Associated with Turner Syndrome

34%   Aortic valve anomalies - bicuspid aortic valve
19%   Aortic arch abnormalities - coarctation of the aorta
8%     Systemic venous abnormalities
5%     Ventricular septal defect
4%     Pulmonary venous abnormalities
3.5%  Hypoplastic left heart and single ventricle
1.7%  Mitral valve abnormalities
1.7%  Atrial septal defect
1.6%  Coronary artery abnormalities

Cramer JW, Bartz PJ, Simpson PM, Zangwill SD.
Pediatr Cardiol. 2013 Aug 10.
PMID 23933717

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